JIM 2024; 1 (4): e628
DOI: 10.61012_202411_628

The current use of alternative dietary protocols for glycogen storage disease type III among Italian dietitians

Topic: Dietetics   Category:

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Abstract

Objective: To investigate the use of Alternative Dietary Protocols (ADPs) for treating Glycogen Storage Disease Type III (GSD III) by Italian dietitians and nutritionists working in Inherited Metabolic Diseases (IMDs).


Materials and Methods: A 16-question online survey was distributed to all Italian members of the Nutrition and Dietetic working group of the Italian Society for the Study of Hereditary Metabolic Diseases and Newborn Screening (SIMMESN), addressing ADPs usage, specific protocols, special medical foods, medium-chain triglyceride supplements, hydration, vitamins, and minerals. The survey also inquired about side effects, night-time meals, cornstarch use and emergency protocols.


Results: All dietitians/nutritionists reported using at least one ADPs for both adult and paediatric patients. The most common protocol was a high-fat, high-protein diet (66%), followed by the Modified Atkins Diet (MAD) (33%). Less frequently, ketogenic or high-fat diets were implemented. These dietary changes extended fasting intervals and reduced or eliminated night-time meals and cornstarch use without any reported hypoglycemic events.


Conclusions: This is the first study in Italy to examine the use of ADPs for GSD III. Further research is needed to provide clinical evidence on the efficacy of these dietary strategies in managing GSD III.

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To cite this article

The current use of alternative dietary protocols for glycogen storage disease type III among Italian dietitians

JIM 2024; 1 (4): e628
DOI: 10.61012_202411_628

Publication History

Submission date: 22 Oct 2024

Revised on: 12 Nov 2024

Accepted on: 25 Nov 2024

Published online: 29 Nov 2024